CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L135* (c.404T>A)

L135* (c.404T>A)

CIViC ID: 1769 · Gene: VHL

Variant Summary

Also known as
C.404T>A,L135X,LEU135TER
HGVS
ENST00000256474.2:c.404T>A,NC_000003.11:g.10188261T>A,NM_000551.3:c.404T>A,NP_000542.1:p.Leu135Ter
Variant Type(s)
stop_gained
Evidence Items
2

Evidence Level Distribution

Level C: 2

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L135* (c.404T>A).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease3
CPredisposingSupportsUncertain SignificanceVon Hippel-Lindau Disease3