CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L158fs (c.471dupT)

L158fs (c.471dupT)

CIViC ID: 1783 · Gene: VHL

Variant Summary

Also known as
C.685INST
HGVS
NC_000003.11:g.10191478dup,NC_000003.12:g.10149794dup,NM_000551.3:c.471dup,NP_000542.1:p.Leu158SerfsTer16,ENST00000256474.2:c.471dup,ENSP00000256474.2:p.Leu158SerfsTer16
Variant Type(s)
frameshift_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L158fs (c.471dupT).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingVon Hippel-Lindau Disease2