CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/N131fs (c.390_391del)

N131fs (c.390_391del)

CIViC ID: 1800 · Gene: VHL

Variant Summary

Also known as
C.390_391DELTA,ASN131PRO,N131PFS*3,ASN131PROFSTER3
HGVS
ENST00000256474.2:c.390_391delTA,NC_000003.11:g.10188247_10188248del,NC_000003.12:g.10146563_10146564del,NM_000551.3:c.390_391delTA,NP_000542.1:p.Asn131fs,NP_000542.1:p.Asn131ProfsTer3
Variant Type(s)
minus_2_frameshift_variant
Evidence Items
2

Evidence Level Distribution

Level C: 2

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = N131fs (c.390_391del).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsUncertain SignificanceVon Hippel-Lindau Disease3
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease3