CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/V181fs (c.540_543del)

V181fs (c.540_543del)

CIViC ID: 1847 · Gene: VHL

Variant Summary

Also known as
VAL181FS,C.540_543DELCGTC,RS869025664
HGVS
NC_000003.11:g.10191547_10191550del,NC_000003.12:g.10149863_10149866del,NM_000551.3:c.540_543del,NP_000542.1:p.Val181fs
Variant Type(s)
frameshift_truncation,minus_1_frameshift_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = V181fs (c.540_543del).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease3