CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/Q164R (c.491A>G)

Q164R (c.491A>G)

CIViC ID: 1856 · Gene: VHL

Variant Summary

Also known as
C.491A>G,GLN164ARG,RS267607170
HGVS
NM_000551.3:c.491A>G,NP_000542.1:p.Gln164Arg,NC_000003.11:g.10191498A>G,ENST00000256474.2:c.491A>G
Variant Type(s)
missense_variant
Evidence Items
3

Evidence Level Distribution

Level C: 3

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = Q164R (c.491A>G).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease4
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease4
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2