CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L169P (c.506T>C)

L169P (c.506T>C)

CIViC ID: 1887 · Gene: VHL

Variant Summary

Also known as
C.506T>C,LEU169PRO,RS1131690962
HGVS
NM_000551.3:c.506T>C,NP_000542.1:p.Leu169Pro,NC_000003.11:g.10191513T>C,ENST00000256474.2:c.506T>C
Variant Type(s)
missense_variant
Evidence Items
3

Evidence Level Distribution

Level C: 3

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L169P (c.506T>C).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease4
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2
CPredisposingSupportsUncertain SignificanceVon Hippel-Lindau Disease1