CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L178R (c.533T>G)

L178R (c.533T>G)

CIViC ID: 1888 · Gene: VHL

Variant Summary

Also known as
C.533T>G,LEU178ARG
HGVS
ENST00000256474.2:c.533T>G,NC_000003.11:g.10191540T>G,NM_000551.3:c.533T>G,NP_000542.1:p.Leu178Arg
Variant Type(s)
missense_variant
Evidence Items
2

Evidence Level Distribution

Level C: 2

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L178R (c.533T>G).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease4
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2