CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L198Q (c.593T>A)

L198Q (c.593T>A)

CIViC ID: 2010 · Gene: VHL

Variant Summary

Also known as
C.593T>A,LEU198GLN
HGVS
ENST00000256474.2:c.593T>A,NC_000003.11:g.10191600T>A,NM_000551.3:c.593T>A,NP_000542.1:p.Leu198Gln
Variant Type(s)
missense_variant
Evidence Items
2

Evidence Level Distribution

Level C: 2

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L198Q (c.593T>A).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease3
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2