CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/Splice Site (c.464-1G>C)

Splice Site (c.464-1G>C)

CIViC ID: 2077 · Gene: VHL

Variant Summary

Also known as
C.464-1G>C,RS5030817,IVS2-1G>C
HGVS
NM_000551.3:c.464-1G>C,NC_000003.11:g.10191470G>C,ENST00000256474.2:c.464-1G>C,NP_000542.1:p.=,NC_000003.12:g.10149786G>C
Variant Type(s)
splice_acceptor_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = Splice Site (c.464-1G>C).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingVon Hippel-Lindau Disease2