CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/Splice Region (c.340+5G>C)

Splice Region (c.340+5G>C)

CIViC ID: 2104 · Gene: VHL

Variant Summary

Also known as
C.340+5G>C,C.533+5G>C,IVS1+5G>C
HGVS
NM_000551.3:c.340+5G>C,NC_000003.11:g.10183876G>C,ENST00000256474.2:c.340+5G>C,NP_000542.1:p.?,NC_000003.12:g.10142192G>C
Variant Type(s)
intron_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = Splice Region (c.340+5G>C).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2