CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/A56fs (c.166dup)

A56fs (c.166dup)

CIViC ID: 2144 · Gene: VHL

Variant Summary

Also known as
C.165DUP,C.165_166DUPG,A56GFS*76 (C.166DUP)
HGVS
NP_000542.1:p.Ala56fs,NC_000003.11:g.10183697dup,NC_000003.12:g.10142013dup,NM_000551.3:c.166dup
Variant Type(s)
plus_1_frameshift_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = A56fs (c.166dup).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingVon Hippel-Lindau Disease3