CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/L129P (c.386T>C)

L129P (c.386T>C)

CIViC ID: 2508 · Gene: VHL

Variant Summary

Also known as
L129P (C.386T>G)
HGVS
ENST00000256474.2:c.386T>C,NC_000003.11:g.10188243T>C,NM_000551.3:c.386T>C,NP_000542.1:p.Leu129Pro,ENSP00000256474.2:p.Leu129Pro,NC_000003.12:g.10146559T>C
Variant Type(s)
missense_variant
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = L129P (c.386T>C).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease2