CIViC Compass
Research use only — not FDA-cleared, not medical advice. Always consult FDA-approved labeling and a qualified clinician.
CIViC Variants/A56FS (c.164_165insG)

A56FS (c.164_165insG)

CIViC ID: 771 · Gene: VHL

Variant Summary

Also known as
164INSG,C.164_165INSG,377_378INSG
HGVS
NP_000542.1:p.Ala56fs,NP_000542.1:p.Ala56GlyfsTer74,NM_000551.2:c.164_165insG,NC_000003.11:g.10183695_10183696insG,NC_000003.11:g.10183697dupG
Variant Type(s)
frameshift_truncation
Evidence Items
1

Evidence Level Distribution

Level C: 1

Evidence Items

Showing CIViC evidence rows where gene = VHL and variant = A56FS (c.164_165insG).

LevelTypeDirectionSignificanceDiseaseDrugsRating
CPredisposingSupportsPredispositionVon Hippel-Lindau Disease3